Guideline for the diagnosis and management of the rare coagulation disorders: a United Kingdom Haemophilia Centre Doctors' Organization guideline on behalf of the British Committee for Standards in Haematology

Br J Haematol. 2014 Nov;167(3):304-26. doi: 10.1111/bjh.13058. Epub 2014 Aug 6.
No abstract available

Keywords: bleeding disorder; factor concentrate; molecular genetics; rare coagulation disorders.

Publication types

  • Practice Guideline

MeSH terms

  • Adult
  • Afibrinogenemia / diagnosis
  • Afibrinogenemia / epidemiology
  • Afibrinogenemia / genetics
  • Afibrinogenemia / therapy
  • Blood Coagulation Factors / administration & dosage
  • Blood Coagulation Factors / genetics
  • Blood Coagulation Factors / therapeutic use
  • Blood Coagulation Tests
  • Child
  • Coagulation Protein Disorders / diagnosis
  • Coagulation Protein Disorders / epidemiology
  • Coagulation Protein Disorders / genetics
  • Coagulation Protein Disorders / therapy
  • Disease Management
  • Female
  • Fibrinogen / genetics
  • Fibrinogen / therapeutic use
  • Hemorrhage / prevention & control
  • Hemorrhagic Disorders* / diagnosis
  • Hemorrhagic Disorders* / epidemiology
  • Hemorrhagic Disorders* / genetics
  • Hemorrhagic Disorders* / therapy
  • Humans
  • Male
  • Pregnancy
  • Pregnancy Complications, Hematologic / therapy
  • Recombinant Proteins / therapeutic use

Substances

  • Blood Coagulation Factors
  • Fibrinogen
  • Recombinant Proteins