Type of alpha (IV) chains | Distribution in tissues |
Alpha-1 | All tissues (Ubiquitous) |
Alpha-2 | All tissues (Ubiquitous) |
Alpha-3 | Kidney (GBM, distal TBM), Eye (Descemet membrane, Bruch membrane, anterior lens capsule), Lungs, Ear (cochlea) |
Alpha-4 | Kidney (GBM, distal TBM), Eye (Descemet membrane, Bruch membrane, anterior lens capsule), Lungs, Ear (cochlea) |
Alpha-5 | Kidney (GBM, distal TBM), Eye (Descemet membrane, Bruch membrane, anterior lens capsule), Lungs, Ear (cochlea) |
Alpha-6 | Kidney (Distal TBM), Skin (epidermal basement membrane) |
GBM, glomerular basement membrane; TBM, tubular basement membrane.