RT Journal Article SR Electronic T1 IgG4-related lung disease as a differential diagnosis of a lymphoproliferative disease: atypical presentation of an atypical disease JF BMJ Case Reports JO BMJ Case Reports FD BMJ Publishing Group Ltd SP e247295 DO 10.1136/bcr-2021-247295 VO 15 IS 1 A1 Vargas, Camilo A1 Velásquez, Carolina A1 Mancilla, Edgardo A1 Aracena, Joaquín YR 2022 UL http://casereports.bmj.com/content/15/1/e247295.abstract AB IgG4-related disease (IgG4-RD) is an immunomodulated inflammatory disease that usually affects the pancreas and parotid glands. Although lung involvement is rare, it has been recently reported and could mimic various other diagnoses. We present a case of IgG4-RD whose symptoms and images raised the suspicion of a malignant lymphoproliferative lung neoplasm. It is imperative to differentiate both diseases, since their treatment and prognosis vary.