PT - JOURNAL ARTICLE AU - Gargi Pandey AU - Fiona McClenaghan AU - Robert Nash TI - Primary presentation of sarcoidosis with profound bilateral sensorineural hearing loss AID - 10.1136/bcr-2021-244140 DP - 2021 Aug 01 TA - BMJ Case Reports PG - e244140 VI - 14 IP - 8 4099 - http://casereports.bmj.com/content/14/8/e244140.short 4100 - http://casereports.bmj.com/content/14/8/e244140.full SO - BMJ Case Reports2021 Aug 01; 14 AB - We present a case of a 7-year-old Afro-Caribbean girl presenting with rapidly progressive bilateral sensorineural hearing loss. She was found to have an elevated Angiotensin converting enzyme (ACE) and mediastinal lymphadenopathy containing non-caseating granulomas with multinucleate giant cells, in keeping with sarcoidosis. Cranial imaging demonstrated labyrinthitis. She underwent urgent bilateral cochlear implantation with rehabilitation of hearing sufficient to restart education within 1 month.