%0 Journal Article %A Gargi Pandey %A Fiona McClenaghan %A Robert Nash %T Primary presentation of sarcoidosis with profound bilateral sensorineural hearing loss %D 2021 %R 10.1136/bcr-2021-244140 %J BMJ Case Reports %P e244140 %V 14 %N 8 %X We present a case of a 7-year-old Afro-Caribbean girl presenting with rapidly progressive bilateral sensorineural hearing loss. She was found to have an elevated Angiotensin converting enzyme (ACE) and mediastinal lymphadenopathy containing non-caseating granulomas with multinucleate giant cells, in keeping with sarcoidosis. Cranial imaging demonstrated labyrinthitis. She underwent urgent bilateral cochlear implantation with rehabilitation of hearing sufficient to restart education within 1 month. %U https://casereports.bmj.com/content/bmjcr/14/8/e244140.full.pdf