PT  - JOURNAL ARTICLE
AU  - Vaishnavi Divya Nagarajan
AU  - Asha Shenoi
AU  - Lucy Burgess
AU  - Vlad C Radulescu
TI  - Spontaneous pyohaemothorax in a teenager with von Willebrand disease: a case report and review of literature
AID  - 10.1136/bcr-2021-241613
DP  - 2021 Aug 01
TA  - BMJ Case Reports
PG  - e241613
VI  - 14
IP  - 8
4099  - http://casereports.bmj.com/content/14/8/e241613.short
4100  - http://casereports.bmj.com/content/14/8/e241613.full
SO  - BMJ Case Reports2021 Aug 01; 14
AB  - An 18-year-old man with a history of type 3 von Willebrand disease (VWD) presented with a spontaneous pyohaemothorax. Type 3 VWD may present with both mucocutaneous and deep-seated bleeds, such as visceral haemorrhages, intracranial bleeds and haemarthrosis. There have been very few cases described in children of spontaneous pyohaemothorax. Management of this patient was challenging due to risks of bleeding following surgical drainage, requiring constant replacement with von Willebrand factor concentrate, while monitoring factor VIII levels to balance the risks of thrombosis.