RT Journal Article SR Electronic T1 Atypical presentation of peripheral posterior lenticonus and role of multi-modal ocular imaging in its diagnosis and management JF BMJ Case Reports JO BMJ Case Reports FD BMJ Publishing Group Ltd SP e238801 DO 10.1136/bcr-2020-238801 VO 14 IS 2 A1 Rinky Agarwal A1 Vatika Jain A1 Manpreet Kaur A1 Jeewan S Titiyal YR 2021 UL http://casereports.bmj.com/content/14/2/e238801.abstract AB A 6-year-old systemically healthy child presented with visual acuity of 1/60, N18 oculusdextrus (OD), and 6/18, N6 oculus sinister (OS). Slit-lamp biomicroscopy revealed suspicious bilateral inferotemporal pigmented ciliary body (CB) tumour, protruding posterior capsule and temporal posterior subcapsular cataract oculus uterque. Anterior segment optical coherence tomography, ultrasonography, ultrasonic biomicroscopy and Scheimpflug imaging revealed protruding posterior capsule and cortex abutting but not arising from CB suggestive of peripheral pigmented posterior lenticonus with hypermetropia (axial length 20.27 mm OD and 19.97 mm OS). Aberrometry revealed high internal aberrations and low Dysfunctional Lens Index (DLI). Lens aspiration with intraocular lens implantation in the bag OD and contact lens correction OS were undertaken. The child had a postoperative visual gain of 3/60, N18 with improved aberrometric profile OD, and was advised amblyopia therapy. Rarely posterior lenticonus can mimic a CB mass. Multi-modal ocular imaging can aid in its diagnosis and management. DLI may serve as a useful indicator of surgery in such cases.