TY - JOUR T1 - Successful liver transplantation in common variable immune deficiency with reversal of hepatopulmonary syndrome JF - BMJ Case Reports JO - BMJ Case Reports DO - 10.1136/bcr-2018-226095 VL - 12 IS - 4 SP - e226095 AU - Ross Apostolov AU - Marie Sinclair AU - Julie Lokan AU - Peter Angus Y1 - 2019/04/01 UR - http://casereports.bmj.com/content/12/4/e226095.abstract N2 - Common variable immune deficiency (CVID) is a primary immunodeficiency disorder that is associated with abnormal liver function tests, however advanced liver disease is uncommon. Hepatopulmonary syndrome (HPS) is a rare but debilitating complication of CVID-associated liver disease. We report a case of CVID complicated by HPS that was successfully treated with orthotopic liver transplant, with the patient recovering to normal hepatic function and successfully weaning off domiciliary oxygen post-transplantation. ER -