RT Journal Article
SR Electronic
T1 Laryngoceles with airway compromise complicating mucous membrane pemphigoid
JF BMJ Case Reports
FD BMJ Publishing Group Ltd
SP bcr-2018-225316
DO 10.1136/bcr-2018-225316
VO 2018
A1 Wijaya, Carolyn
A1 Morgan, Lucy
A1 Novakovic, Daniel
A1 Riminton, Sean
YR 2018
UL http://casereports.bmj.com/content/2018/bcr-2018-225316.abstract
AB Mucous membrane pemphigoid (MMP) encompasses a group of autoantibody-mediated, subepithelial blistering diseases, which primarily affect mucosal surfaces including oral, ocular, skin, genital, nasopharyngeal and oesophageal sites. We present a first description of laryngoceles as a manifestation of mucous membrane pemphigoid resulting in dynamic airway closure. Mucosal injury at other sites had previously resulted in pathergy and localised cicatrisation. We discuss successful combined medical and transcutaneous surgical intervention designed to avoid tracheostomy and minimise iatrogenic laryngeal cicatrisation.