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CASE REPORT
Parry-Romberg syndrome in a patient with scleroderma
  1. Chii Yang Kuah1,
  2. Elena Koleva1,
  3. Jaslyn Ju Lia Gan2,
  4. Tahir Iqbal1
  1. 1Department of Dermatology, Southend University Hospital NHS Foundation Trust, Westcliff-on-Sea, UK
  2. 2General Surgery, Lister Hospital, Stevenage, Hertfordshire, UK
  1. Correspondence to Dr Chii Yang Kuah, james.kcy{at}hotmail.com

Summary

Parry-Romberg syndrome (PRS) is characterised by progressive but self-limiting facial hemiatrophy. We describe a 48-year-old woman with a 3-year history of gradually worsening right facial hemiatrophy on a background of scleroderma. Her initial primary concern was alopecia. Within the last year, there was greater prominence of her right zygoma and hyperpigmentation on her forearms and left neck. She also had worsening headaches and neck stiffness in the mornings. A clinical diagnosis of PRS was made and she was subsequently treated with a course of methotrexate. She is due to be followed up by dermatology, rheumatology and maxillofacial surgery with the aim of reconstructive surgery once her symptoms stabilise.

  • dermatology
  • connective tissue disease
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Footnotes

  • Contributors CYK, TI and EK had the idea for the article. CYK and JJLG performed the literature search and wrote the article. TI gave expert opinion and reviewed the article. CYK, EK and TI managed the case. All authors approved the final version of this manuscript.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Patient consent Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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