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Unusual association of diseases/symptoms
CASE REPORT
Laryngoceles with airway compromise complicating mucous membrane pemphigoid
  1. Carolyn Wijaya1,2,
  2. Lucy Morgan1,3,
  3. Daniel Novakovic1,
  4. Sean Riminton1,2
  1. 1Sydney Medical School, University of Sydney, Sydney, New South Wales, Australia
  2. 2Immunology Department, Concord Repatriation General Hospital, Concord, New South Wales, Australia
  3. 3Respiratory Department, Concord Repatriation General Hospital, Concord, New South Wales, Australia
  1. Correspondence to Dr Carolyn Wijaya, Carolyn.Wijaya{at}health.nsw.gov.au

Summary

Mucous membrane pemphigoid (MMP) encompasses a group of autoantibody-mediated, subepithelial blistering diseases, which primarily affect mucosal surfaces including oral, ocular, skin, genital, nasopharyngeal and oesophageal sites. We present a first description of laryngoceles as a manifestation of mucous membrane pemphigoid resulting in dynamic airway closure. Mucosal injury at other sites had previously resulted in pathergy and localised cicatrisation. We discuss successful combined medical and transcutaneous surgical intervention designed to avoid tracheostomy and minimise iatrogenic laryngeal cicatrisation.

  • immunology
  • ear, nose and throat/otolaryngology

https://doi.org/10.1136/bcr-2018-225316

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    Footnotes

    • Contributors CW has contributed by drafting and editing the case report, as well as acquisition of relevant images and final approval. LM was involved in the patient’s care, analysis of data, revision of case report and final approval. DN was involved in the patient’s care, procurement of images, revision of case report and final approval. SR was involved in the patient’s care and contributed to the conception, drafting and revision of the case report, as well as final approval.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Competing interests None declared.

    • Patient consent Obtained.

    • Provenance and peer review Not commissioned; externally peer reviewed.