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CASE REPORT
Disabling pansclerotic morphoea of childhood
  1. Indirakshi Jamalpur1,
  2. Harikrishna Reddy Mogili2,
  3. Abhilash Koratala3
  1. 1Department of Dermatology, Kurnool Medical College, Kurnool, Andhra Pradesh, India
  2. 2Department of Medicine, Sri Venkateswara Institute of Medical Sciences, Tirupati, Andhra Pradesh, India
  3. 3Department of Nephrology, University of Florida College of Medicine, Gainesville, Florida, USA
  1. Correspondence to Dr Abhilash Koratala, akoratsla{at}ufl.edu

Summary

Disabling pansclerotic morphoea (DPM) of childhood is a severe and often fatal variant of deep morphoea. It usually starts in childhood and rarely seen in adults. The course of the disease is progressive with lifelong morbidity in the form of joint contractures and immobility. The causes of mortality include complications such as sepsis, gangrene and cardiopulmonary involvement. Herein, we discuss the case of a 15-year-old girl with limb deformity and finger contractures, that is, bone involvement. The diagnosis of DPM of childhood was fortuitously made after the correction of limb deformity, when the patient was seen in the dermatology department for evaluation of skin discolouration on the thighs.

  • dermatology
  • neurology
  • pathology

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Footnotes

  • Contributors IJ and HRM drafted the initial version of the manuscript and procured the images. AK revised the manuscript for critically important intellectual content and prepared the final version.

  • Competing interests None declared.

  • Patient consent Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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