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Severe panniculitis and polyarthritis caused by acinar cell carcinoma arising from an ectopic pancreas
  1. Marc Plier1,
  2. Patrick Durez1,
  3. Mina Komuta2,
  4. Alexandros Raptis2
  1. 1Department of Rheumatology, Cliniques Universitaires Saint-Luc, Bruxelles, Belgium
  2. 2Department of Pathology, Cliniques Universitaires Saint-Luc, Bruxelles, Belgium
  1. Correspondence to Dr Marc Plier, pliermarc{at}


The pancreatitis, panniculitis and polyarthritis (PPP) syndrome is a rare condition caused by pancreatic diseases, such as acute or chronic pancreatitis or pancreatic carcinoma. We report the first case of PPP syndrome caused by metastatic acinar cell carcinoma from an ectopic pancreas. The symptoms were successfully managed by the treatment of the metastatic carcinoma. Pancreatic cytosteatonecrosis should be always considered in a patient who is showing symptoms of panniculitis and polyarthritis.

  • pancreatic cancer
  • musculoskeletal syndromes

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  • Contributors MP and AR contributed equally to the writing of this paper. PD and MK helped for writing the paper.

  • Competing interests None declared.

  • Patient consent Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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