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CASE REPORT
Congenital pulmonary airway malformation (CPAM) with initial presentation in an adult: a rare presentation of a rare disease
  1. Mohannad Abu Omar1,
  2. Emily Tylski2,
  3. Mouhanna Abu ghanimeh2,
  4. Ashraf Gohar1
  1. 1University of Missouri-Kansas City, Pulmonary/Critical Care, Kansas City, Missouri, USA
  2. 2Department of Internal medicine, University of Missouri-Kansas City, Kansas City, Missouri, USA
  1. Correspondence to Dr Mohannad Abu Omar, muhannadabuomar{at}yahoo.com

Summary

Congenital pulmonary airway malformation (CPAM) is a rare congenital abnormality with unknown exact aetiology or clear genetic association. It is characterised by a failure of bronchial development and localised glandular overgrowth. Typically, it is diagnosed on prenatal ultrasound, only infrequently in children, and even less commonly in adults. We present a case of a 25-year-old man, with no previous lung diseases who presented with right-sided chest pain, fever and cough suggestive of pulmonary infection. Chest imaging, including CT scan, showed a large focal cystic mass within the right lower lobe along with ground glass opacities suggestive of CPAM. He was started on intravenous antibiotics. Bronchoscopy showed a large amount of pus in the right lung and bronchoalveolar lavage confirmed the microbiological diagnosis of methicillin-resistant Staphylococcus aureus. He improved with antibiotic treatment. He was discharged with 6-week course of antibiotics and follow-up afterward.

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