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Sturge-Weber syndrome type 3 manifesting as ‘Status migrainosus’
  1. Philip Richard Jordan1,
  2. Mehtab Iqbal2,
  3. Manish Prasad3
  1. 1Department of Paediatrics, University Hospitals of Leicester NHS Trust, Leicester, UK
  2. 2Department of Paediatric Neurology, University Hospital of Leicester NHS Trust, Leicester, UK
  3. 3Department of Paediatrics, Nottingham University Hospitals Trust, Nottingham, UK
  1. Correspondence to Dr Mehtab Iqbal, drmehtabch{at}


Sturge-Weber syndrome (SWS) is a rare neurocutaneous syndrome characterised by facial naevus and leptomeningeal angiomatosis resulting in neurological and ophthalmological complications. In its rare variant, SWS type 3, the clinical hallmark of facial naevus is absent which poses a diagnostic challenge. Here, we present an interesting case of SWS type 3 where a child presented twice with prolonged severe unilateral headache mimicking migraine status followed on both occasions with focal seizures. He developed a dense right-sided homonymous hemianopia, and an urgent brain MRI scan was performed which pointed towards the diagnosis of SWS type 3.

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  • Contributors PRJ and MI performed literature research and wrote the article. MP helped in final drafting the article.

  • Competing interests None declared.

  • Patient consent Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.