Article Text

PDF
CASE REPORT
Rapunzel syndrome: a rare cause of hypoproteinaemia and review of literature
  1. Waqas Ullah1,
  2. Kaiser Saleem2,
  3. Ejaz Ahmad3,
  4. Faiz Anwer4
  1. 1University of Arizona, Tucson, Arizona, USA
  2. 2Griffin Hospital, Derby, Connecticut, USA
  3. 3Department of Medical Education, Griffin Hospital, Derby, Connecticut, USA
  4. 4Department of Hematology Oncology, University of Arizona Medical Center, Tucson, Arizona, USA
  1. Correspondence to Dr Faiz Anwer, anwerf{at}email.arizona.edu

Summary

Rapunzel syndrome is an extremely rare condition associated with trichophagia (hair eating disorder) secondary to a psychiatric illness called trichotillomania (hair-pulling behaviour). It is most commonly seen in children and adolescents. Untreated cases can lead to a number of complications. We present a case of a middle-aged woman with sudden intractable vomiting and constipation associated with bilateral pedal oedema and significant weight loss. Laboratory investigations revealed low serum protein levels. Laparotomy was performed, and a hairball was removed from her stomach and ileum. The patient was managed with the help of a psychiatrist and was given nutritional support. We performed a comprehensive search and summarised data for a total of 88 cases. No time or language limit was placed. The purpose of this discussion is to highlight the clinical spectrum of Rapunzel syndrome and also to report its rare association with hypoproteinaemia.

Statistics from Altmetric.com

Request Permissions

If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.