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Moyamoya syndrome in sickle cell anaemia: a cause of recurrent stroke
  1. Deanne Soares1,
  2. Richard Bullock1,
  3. Susanna Ali2
  1. 1Departments of Surgery, Radiology, Anaesthetics and Intensive Care, Radiology Section, University of the West Indies, Kingston, Jamaica
  2. 2Sickle Cell Unit, TMRI, University of the West Indies, Kingston, Jamaica
  1. Correspondence to Dr Deanne Soares, deanne_soares{at}


We report a case with interesting imaging findings as well as an unfortunate but not unexpected clinical outcome. Our patient, an 8-year-old Jamaican boy of Afro-Caribbean descent with homozygous sickle cell disease, presented with left-sided upper limb weakness. He had a history of recurrent cerebrovascular accidents and transient ischaemic attacks beginning at 4 years of age. MRI revealed old bilateral infarctions and the ivy sign on fluid-attenuated inversion recovery sequences. MR angiography demonstrated numerous collaterals, most apparently arising from the left internal carotid, consistent with moyamoya syndrome. The patient had a full recovery and remained well for almost 2 years when he suffered another stroke.

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