Description

A 30-year-old male presented with a 15-year history of proximal weakness and decreased temperature sensation in both upper limbs. There was no history to suggest a hereditary connective tissue disorder, and no prior trauma. On examination, he had lateral winging of the scapula (WOS) with the superior angle displaced laterally (figure 1), mild weakness of bilateral upper extremities, reduced pain and temperature sensation in dermatomes C2 to T3, and normal proprioception, while tendon reflexes were absent in the upper limbs and brisk in the lower limbs, …