Article Text

Download PDFPDF
Spontaneous pneumothorax as manifestation of Marfan syndrome
  1. Carolina Viveiro,
  2. Patricia Rocha,
  3. Cristiana Carvalho,
  4. Maria Manuel Zarcos
  1. Department of Pediatria, Centro Hospitalar de Leiria–Pombal, Leiria, Portugal
  1. Correspondence to Dr Cristiana Carvalho, cristiana.mafalda{at}


The authors describe a 16-year-old boy, previously healthy, who was admitted to our hospital for left-sided spontaneous pneumothorax. On physical examination he presented with marfanoid habitus. Pneumothorax was managed conservatively with resolution. Four months later he had a recurrence of left-sided pneumothorax and 1 week after that he presented with contralateral pneumothorax. He underwent video-assisted thoracoscopic surgery twice for bullectomy and pleurodesis. No further recurrence was stated. Additional investigation showed a prolapsed cardiac mitral valve and Marfan syndrome was confirmed genetically.

View Full Text

Statistics from

Request Permissions

If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.