Description

Single ventricle (SV) defects, including common inflow of both the atria emptying into one ventricle, occur at an incidence of 0.05–0.1/10 000 live-births.1 Common atrium is a rare variety of interatrial communication which forms a type of endocardial cushion defect characterised by deficient atrial septum, the vestigial remnants sometimes remain as diaphanous strands of tissue.2 ,3 Common atrium is very rarely seen in patients with SV.3 In patients with common atrium and SV, there is mixing of arterial and venous blood in the common cardiac chamber which causes severe cyanosis and hypoxia in these patients.3 ,4

We report the case of a 6-month-old female baby who presented with central cyanosis, dyspnoea along with difficulty in feeding, fatigue and irritability since the neonatal period. She was the result of a full-term, caesarean delivery with an uneventful antenatal and perinatal course with no other obvious external malformations. She was the …