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Rare disease
Pulmonary lymphangioleiomyomatosis associated with retroperitoneal lymphangioleiomyomas
  1. Anastasia Oikonomou1,
  2. Argyris Tzouvelekis2,
  3. Petros Zezos3,
  4. Demostehenes Bouros2,
  5. Panos Prassopoulos1
  1. 1Radiology Department, University Hospital of Alexandroupolis, Democritus University of Thrace, Alexandroupolis, Greece
  2. 2Pneumonology Department, University Hospital of Alexandroupolis, Democritus University of Thrace, Alexandroupolis, Greece
  3. 3Gastroenetrology Department, University Hospital of Alexandroupolis, Democritus University of Thrace, Alexandroupolis, Greece
  1. Correspondence to Dr Anastasia Oikonomou, aoikonom{at}med.duth.gr

Summary

A 36-year-old woman presented with worsening symptoms of abdominal pain, diarrhoea, low fever, dyspnoea on exertion and bilateral leg during the last 2 months. Chest radiograph showed mild diffuse reticular pattern with preserved lung volumes. Lung high resolution CT disclosed multiple thin-walled lung cysts throughout the lungs bilaterally with no zonal predominance and with normal intervening parenchyma and abdominal CT revealed bilateral retrocrural and retroperitoneal hypodense masses. Imaging findings were consistent with lymphangioleiomyomatosis.

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Footnotes

  • Competing interests None.

  • Patient consent Obtained.

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