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Rare disease
Excellent response of malignant peripheral nerve sheath tumour of retroperitoneum to radiation therapy
  1. Ali Akhavan1,
  2. Fariba Binesh2,
  3. Fazlollah Ghannadi3,
  4. Hossein Navabii4
  1. 1Department of Radiotherapy, Shahid Sadoghi University of Medical Science, Yazd, Islamic Republic of Iran
  2. 2Department of Pathology, Shahid Sadoghi University, Yazd, Islamic Republic of Iran
  3. 3Research Department, Isfahan University of Medicine, Isfahan, Islamic Republic of Iran
  4. 4Shahid Sadoghi University of Medical Scince, Yazd, Islamic Republic of Iran
  1. Correspondence to Dr Ali Akhavan, ali52akhavan{at}yahoo.com.

Summary

Malignant peripheral nerve sheath tumours are high-grade sarcomas originating from Schwann cells or nerve sheath cells. Most of these tumours are associated with major nerves of the body wall and extremities. The lower extremity and the retroperitoneum are the most common sites. Surgery is the cornerstone of treatment, however, radiation therapy is usually used as an adjuvant treatment. In this paper we present a 57-year-old Iranian woman with malignant peripheral nerve sheath tumour of retroperitoneum who was operated subtotally and then underwent radiation therapy which led to disappearance of all gross residual disease.

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