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Rare disease
Binder’s syndrome
  1. Upendra Jain1,
  2. Gagan Thakur2,
  3. Amitabh Kallury1
  1. 1Department of Orthodontia, People’s College of Dental Sciences and Research Centre, Bhopal, Madhya Pradesh, India
  2. 2Department of Oral and Maxillofacial Surgery, People’s College of Dental Sciences and Research Centre, Bhopal, Madhya Pradesh, India
  1. Correspondence to Dr Gagan Thakur, drgagan05{at}yahoo.com

Summary

Binder syndrome or maxillonasal dysplasia is an uncommon developmental anomaly affecting primarily the anterior part of the maxilla and nasal complex. The characteristic findings are a failure of development in the premaxillary area with associated deformities of the nasal skeleton and the overlying soft tissues. Affected individuals typically have an unusually flat, underdeveloped midface (midfacial hypoplasia), with an abnormally short nose and flat nasal bridge, underdeveloped upper jaw, relatively protruding lower jaw and/or a ‘reverse overbite’ (or class III malocclusion). A 16-year-old female reported to clinic with chief complaint of facial deformity, on examination patient had classical feature of maxillonasal dysplasia. A brief review of the condition and the proposed multi-disciplinary treatment plan is discussed.

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Footnotes

  • Competing interests None.

  • Patient consent Obtained.

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