Article Text

Learning from errors
Congenital laryngomucocoele: a rare cause for CHAOS
  1. Manuel Sousa Cunha1,
  2. Patrícia Janeiro1,
  3. Rosário Fernandes2,
  4. Helena Carreiro1,
  5. Ricardo Laurini3
  1. 1
    Hospital Fernando Fonseca, Pediatrics, IC 19, Amadora, 2720-276, Portugal
  2. 2
    Hospital Fernando Fonseca, Anatomia Patológica, IC 19, Amadora, 2720-276, Portugal
  3. 3
    University Hospital Lund, OB/GYN - Developmental Pathology, University Hospital Lund, Lund, 221 85, Sweden
  1. manuelsousacunha{at}


Congenital high airway obstruction syndrome (CHAOS) is a rare but life-threatening condition that results from the obstruction of the upper airways.

We describe a female newborn, from a Grávida II, Para 0, 36-year-old woman, with a routine ultrasound at 30 weeks’ gestation that showed polyhydramnios. She delivered a live-born female baby at 36 weeks without any dismorphic features but with respiratory distress. Attempts at endotracheal intubation were unsuccessful due to the presence of a mass obstructing the larynx. The reanimation process was stopped after 20 minutes. Post-mortem examination demonstrated the presence of a total occlusion of the larynx by a laryngomucocoele. Laryngocele, a congenital cyst of the larynx, occurs rarely and hardly ever as a cause of CHAOS. What is more, laryngomucocoele has not been previously reported as a cause of CHAOS. These conditions represent a neonatal emergency with reserved prognosis unless diagnosed antenatally allowing for a programmed ex utero intrapartum treatment (EXIT) by performing tracheostomy while maintaining the placental circulation.

View Full Text

Statistics from


  • Competing interests: none.

Request Permissions

If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.