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Pathology
Extraconal orbital craniopharyngioma
  1. Soundarya Samskruthi Koyya1,
  2. Rakesh Kumar Gupta2,
  3. Anil Sharma3 and
  4. Saroj Pati4
  1. 1Pathology and Lab Medicine, AIIMS Raipur, Raipur, Chhattisgarh, India
  2. 2Pathology, AIIMS Raipur, Raipur, Chhattisgarh, India
  3. 3Department of Neurosurgery, AIIMS Raipur, Raipur, Chhattisgarh, India
  4. 4Department of Radiodiagnosis, AIIMS Raipur, Raipur, Chhattisgarh, India
  1. Correspondence to Dr Rakesh Kumar Gupta; rakesh.newjobi{at}gmail.com

Abstract

A female, in her 60s, presented with pain and swelling of the right eye for 3 years. The radiological work-up revealed an extraconal solid-cystic orbital tumour suggestive of an epidermoid cyst. The patient underwent supraorbital craniotomy with a gross total excision of the tumour. An intraoperative diagnosis was sought, which on both squash smear and frozen section showed features of craniopharyngioma (CP), later confirmed on paraffin sections and immunohistochemistry. The orbit is a very rare site for ectopic CP, with only two cases reported in the literature. Many theories have been proposed to explain the occurrence of CP at ectopic sites. This report aims to provide insight into the different hypotheses of the pathogenesis of ectopic CP through a review of the literature.

  • Neurooncology
  • Neuroopthalmology
  • CNS cancer
  • Ophthalmology
  • Pathology

https://doi.org/10.1136/bcr-2023-258652

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    Footnotes

    • X @Soundarya Samskruthi, @NewjobiRakesh

    • Contributors The following authors were responsible for drafting of the text, sourcing and editing of clinical images, investigation results, drawing original diagrams and algorithms, and critical revision for important intellectual content: AS, RKG, SSK. The following authors gave final approval of the manuscript: AS, RKG, SSK, SP. RKG is responsible for the overall content and act as guarantor.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Case reports provide a valuable learning resource for the scientific community and can indicate areas of interest for future research. They should not be used in isolation to guide treatment choices or public health policy.

    • Competing interests None declared.

    • Provenance and peer review Not commissioned; externally peer reviewed.