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Case Reports: Rare disease
Rare Extranodal Manifestation of Rosai-Dorfman Disease Presenting as Nasal Obstruction and its Management
  1. Ting Jie Oui1,2,
  2. Farah Dayana Zahedi1,2,
  3. Salina Husain1,2 and
  4. Aneeza Khairiyah Wan Hamizan1,2
  1. 1Department of Otorhinolaryngology-Head and Neck Surgery, Faculty of Medicine, Universiti Kebangsaan Malaysia, Kuala Lumpur, Kuala Lumpur, Malaysia
  2. 2Department of Otorhinolaryngology-Head and Neck Surgery, Hospital Canselor Tuanku Muhriz, Kuala Lumpur, Kuala Lumpur, Malaysia
  1. Correspondence to Associate Professor Farah Dayana Zahedi; farahdayana{at}ukm.edu.my

Abstract

Rosai-Dorfman disease (RDD) is a rare and benign lymphoproliferative disorder that commonly presents as painless, bilateral neck swelling. Extranodal presentations are considered rare, but the most common extranodal locations involved include skin, subcutaneous followed by nasal/paranasal sinuses. Although it is a benign condition, it may be mistaken as a malignant lesion and requires a biopsy for diagnostic confirmation. In this study, we report a rare case of RDD with bilateral neck node and nasal/paranasal sinus involvement which initially presented with bilateral nasal obstruction. And, we reviewed the management in this unusual case and discussed the helpful role imaging studies play in the further workup and subsequent follow-up to treatment response.

  • Ear, nose and throat/otolaryngology
  • Radiology

http://dx.doi.org/10.1136/bcr-2022-251801

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    Footnotes

    • Contributors TJO is the main author in writing up the case report. FDZ, SH and AKWH advised on the case’s discussion and corrections for the case write-up.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Case reports provide a valuable learning resource for the scientific community and can indicate areas of interest for future research. They should not be used in isolation to guide treatment choices or public health policy.

    • Competing interests None declared.

    • Provenance and peer review Not commissioned; externally peer reviewed.