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Rare presentation of central retinal vein occlusion sparing the superotemporal quadrant in a patient with congenital cardiovascular disease
  1. Rossella Anzidei,
  2. Esraa Ali and
  3. Vasileios Efstathios Konidaris
  1. Ophthalmology, University Hospitals of Leicester NHS Trust, Leicester, UK
  1. Correspondence to Dr Vasileios Efstathios Konidaris; vasiliskon{at}


A young Asian man with a diagnosis of complex congenital heart disease and visceral situs inversus presented to the eye casualty with a recent onset of blurred vision in his left eye. Funduscopic examination of the left eye showed the presence of intraretinal haemorrhages in the inferior and superonasal quadrants, sparing the superotemporal arcade. Optical coherence tomography showed presence of macular oedema and fundus fluorescein angiography confirmed the diagnosis of central retinal vein occlusion sparing the superotemporal branch. Intravitreal antivascular endothelial growth factor treatment was administered, with favourable anatomic and functional outcomes. The presentation of an incomplete central retinal vein occlusion is extremely unusual, especially in a patient with significant cardiac malformation. With the current advances in interventional cardiac procedures, more patients are having longer lifespan and are presenting to ophthalmologists with ocular consequences of circulatory disorders, emphasising the need for multidisciplinary management.

  • ophthalmology
  • macula
  • retina
  • cardiovascular medicine

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  • Contributors RA: conception and design, acquisition of data, analysis and interpretation of data, drafting the article, and approval of the version published. EA: acquisition of data or analysis and interpretation of data, drafting the article, and approval of the version published. VEK: drafting the article and revising it critically. Agreement to be accountable for the article and to ensure that all questions regarding the accuracy or integrity of the article are investigated and resolved. Final approval of the version published.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Case reports provide a valuable learning resource for the scientific community and can indicate areas of interest for future research. They should not be used in isolation to guide treatment choices or public health policy.

  • Competing interests None declared.

  • Provenance and peer review Not commissioned; externally peer reviewed.