You are here

Article Text

Article menu
Download PDFPDF
Case Reports: Rare disease
Primary adenoid cystic carcinoma of the trachea: an elusive diagnosis of chronic dyspnoea
  1. Cecília Caramujo1,
  2. Rafael Moiteiro da Cruz2,3,
  3. Rui Vale Marques4 and
  4. Emanuel Jesus1
  1. 1Department of Medical Oncology, Instituto Português de Oncologia de Coimbra Francisco Gentil EPE, Coimbra, Portugal
  2. 2Department of Pathology, Hospital de Santa Maria, Lisboa, Portugal
  3. 3Universidade de Lisboa Faculdade de Medicina, Lisboa, Portugal
  4. 4Department of Radiotherapy, Instituto Português de Oncologia de Coimbra Francisco Gentil EPE, Coimbra, Portugal
  1. Correspondence to Dr Cecília Caramujo; ce.caramujo{at}gmail.com

Abstract

Primary adenoid cystic carcinoma (ACC) of the trachea is a rare entity, with a 5-year survival between 50% and 80% for resectable cases and 30% in case of unresectable disease. We report a case of a primary ACC on a woman in her 70s that presented with a drawn-out history of dyspnoea. She was diagnosed with an unresectable obstructive tumour of the trachea, which required the placement of a Y-shaped stent. The patient underwent concomitant chemoradiotherapy, with partial response, and is still in follow-up, without evidence of disease progression.

  • Oncology
  • Respiratory cancer
  • Radiotherapy

http://dx.doi.org/10.1136/bcr-2022-250227

Statistics from Altmetric.com

    Request Permissions

    If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.

    View Full Text

    Footnotes

    • Contributors CC: as main author contributed to the acquisition of data and interpretation, planning of the article (conception), writing of the manuscript and revision of contents. RMdC: contributed to the acquisition of data and figures, writing of the manuscript and revision of contents. RVM and EJ: contributed to the acquisition of data and interpretation, writing of the manuscript and revision of contents.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Case reports provide a valuable learning resource for the scientific community and can indicate areas of interest for future research. They should not be used in isolation to guide treatment choices or public health policy.

    • Competing interests None declared.

    • Provenance and peer review Not commissioned; externally peer reviewed.