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Challenges in managing a critically ill patient with decompensated Eisenmenger syndrome
  1. Min Xian Lim1,
  2. Abdul Jabbar Ismail2 and
  3. Tat Boon Yeap2
  1. 1Anaesthesia and Intensive Care Unit, Hospital Queen Elizabeth, Kota Kinabalu, Malaysia
  2. 2Anaesthesiology and Intensive Care Department, Faculty of Medicine and Health Sciences, Universiti Malaysia Sabah, Kota Kinabalu, Sabah, Malaysia
  1. Correspondence to Dr Tat Boon Yeap; boontat{at}


Eisenmenger syndrome (ES) is the most severe form of pulmonary arterial hypertension and is associated with congenital heart disease. ES itself is a challenging condition to manage, further compounded if the patient is critically ill and acutely decompensated. We share our experience of managing a critically ill adult patient with ES who presented with acute decompensation due to sepsis.

  • Anaesthesia
  • Heart failure
  • Congenital disorders

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  • Contributors MXL and AJI comanaged the patient in the ICU. TBY is a coauthor of this manuscript with MXL and AJI.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Case reports provide a valuable learning resource for the scientific community and can indicate areas of interest for future research. They should not be used in isolation to guide treatment choices or public health policy.

  • Competing interests None declared.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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