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Central retinal artery occlusion with cilioretinal sparing in a patient with Eisenmenger syndrome
  1. Abhishek Gupta1,
  2. Prabhakar Singh2,
  3. Sravani Reddy Sanepalli2 and
  4. Amit Raj2
  1. 1Uvea and Retina Services, Department of Ophthalmology, All India Institute of Medical Sciences - Patna, Patna, Bihar, India
  2. 2Department of Ophthalmology, All India Institute of Medical Sciences - Patna, Patna, Bihar, India
  1. Correspondence to Dr Amit Raj; dramitraj{at}


A young boy in his 20s presented with sudden diminution of vision in right eye 2 days ago. Best-corrected visual acuity was hand movement in right eye and 20/20 in left eye. Funduscopy demonstrated diffuse retinal opacification and swelling at the posterior pole with a cherry red spot at the macula. There was sparing of the superonasal macula with a patent cilioretinal artery. OCT showed diffuse inner retinal thickening of the temporal macula. He was diagnosed as central retinal artery occlusion with cilioretinal sparing in right eye. He was a known case of Eisenmenger syndrome secondary to a large congenital ventricular septal defect. Medical history was notable for prominent pulmonary hypertension and shortness of breath on exertion. Physical examination revealed a harsh systolic murmur. Extremities showed digital erythema and severe clubbing. Chest X-ray demonstrated cardiomegaly. Laboratory examination revealed haemoglobin—220 g/L, haematocrit—60%, serum iron—20 µg/dL.

  • eye
  • retina

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  • Contributors AG was involved in the manuscript writing. PS has conceptualised and designed the study. SRS helped in data acquisition. AR involved in review and final draft.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Case reports provide a valuable learning resource for the scientific community and can indicate areas of interest for future research. They should not be used in isolation to guide treatment choices or public health policy.

  • Competing interests None declared.

  • Provenance and peer review Not commissioned; externally peer reviewed.