Article Text
Case report
Primary presentation of sarcoidosis with profound bilateral sensorineural hearing loss
Abstract
We present a case of a 7-year-old Afro-Caribbean girl presenting with rapidly progressive bilateral sensorineural hearing loss. She was found to have an elevated Angiotensin converting enzyme (ACE) and mediastinal lymphadenopathy containing non-caseating granulomas with multinucleate giant cells, in keeping with sarcoidosis. Cranial imaging demonstrated labyrinthitis. She underwent urgent bilateral cochlear implantation with rehabilitation of hearing sufficient to restart education within 1 month.
- ear
- nose and throat/otolaryngology
- general practice/family medicine
- neuro-otology