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  • Management of delayed Sprengel malformation with intracanalar compressive omovertebral bone in a developing country’s neurosurgery unit

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Case report
Management of delayed Sprengel malformation with intracanalar compressive omovertebral bone in a developing country’s neurosurgery unit
  1. Mamadou Salia Diarra1,2,
  2. Mohamed Elhassimi Cisse2,
  3. Aboubacar Sidiki Ndiaye3 and
  4. Izoudine Blaise Koumaré2
  1. 1Neurosurgery, USTTB, Bamako, Mali
  2. 2Neurosurgery, Mere Enfant Hospital, Bamako, Mali
  3. 3Radiology Department, USTTB, Bamako, Mali
  1. Correspondence to Dr Mamadou Salia Diarra; madoucha{at}hotmail.com

Abstract

Sprengel deformity is a congenital abnormality done to the ascent of the scapular bone (which occurs probably between the 5th and 12th weeks of gestation). It can cause cosmetic or functional problems. The aim of our study was to describe this rare deformity, often neglected in our context, and its surgical management. We report a case of a 16-year-old boy with a Sprengel deformity associated with omovertebral intracanalar compressive bone seen on the CT scan. He reported neurological symptoms such as spastic paraparesis and walk disturbances. The bone was resected surgically and physiotherapy was set up. The outcome was good with noticeable neurological improvement of walk and balance, recovery of autonomy. Sprengel deformity is a rare pathology. Surgery must be done early and be adapted to the case.

  • spinal cord
  • neurosurgery
  • head and neck surgery
  • congenital disorders
  • musculoskeletal syndromes

https://doi.org/10.1136/bcr-2021-243203

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    Footnotes

    • Contributors MSD: conduct of the study, surgical procedure and planning, conception and design of the case report, acquisition of data, interpretation of data and clinical follow-up. MEC: conduct of the study, surgical procedure, acquisition of data, design and clinical follow-up. ASN: acquisition of all radiological data (CT scans because of patient’s diability to pay), follow-up and design. IBK: surgical procedure, clinical follow-up and evaluation, design and update.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Competing interests None declared.

    • Provenance and peer review Not commissioned; externally peer reviewed.