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Abdominal compartment syndrome secondary to chronic constipation in MECP2 duplication syndrome
  1. Alyaa Al Ali1,
  2. Ram Singh1,
  3. Guido Filler2 and
  4. Musaab Ramsi3
  1. 1Department of Pediatric Critical Care Medicine, Children’s Hospital, London Health Sciences Centre, University of Western Ontario, London, Ontario, Canada
  2. 2Paediatrics, Univ Western Ontario, London, Ontario, Canada
  3. 3Pediatric Critical Care, Shaikh Khalifa Medical City, Abu Dhabi, UAE
  1. Correspondence to Dr Alyaa Al Ali; alalali.uae{at}


Abdominal compartment syndrome (ACS) is an infrequently encountered life-threatening disorder characterised by elevated abdominal pressure with evidence of new organ dysfunction. It is rarely reported in paediatrics. We describe an extremely unusual presentation of a 13-year-old boy with long-standing constipation who developed ACS complicated by refractory septic shock and multiorgan failure. He was treated with emergent decompressive laparotomy and supportive critical care. This case highlights the need for early diagnosis and timely management of ACS to improve its outcome.

  • paediatrics
  • gastrointestinal surgery

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  • Twitter @picu_ae, @Musaabalramsi

  • Contributors AAA collected the data, performed a literature review and drafted the manuscript. RS clinically managed the case as consultant in charge and reviewed the final report. GF contributed to acquisition and interpretation of the case report, and writing the presentation. MR revised and edited manuscript.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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