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A rare case of retroperitoneal teratoma with obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome
  1. Kazuki Mitani1,
  2. Elena Yukie Uebayashi2,
  3. Hisanori Fujino1 and
  4. Shinichi Sumimoto1
  1. 1Department of Pediatrics, Osaka Red Cross Hospital, Osaka, Japan
  2. 2Department of Pediatric Surgery, Osaka Red Cross Hospital, Osaka, Japan
  1. Correspondence to Dr Kazuki Mitani; mitkazu0816{at}


A 9-month-old girl presented with progressive abdominal distension. Imaging revealed a huge cystic mass in the left retroperitoneum with solid components. The right kidney was absent and hydrometrocolpos was found. Tumour drainage and complete surgical excision were performed. A bulge in the right side of the uterus, suggestive of a uterine anomaly, was seen on laparoscopic observation. Pathology was consistent with teratoma with a small portion of immature neural tissue. The patient was discharged in good condition and was advised regular follow-up.

  • paediatric oncology
  • congenital disorders

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  • Contributors KM and EYU contributed equally to the present work, being co-first authors. All the authors contributed to the management of the case. KM and EYU prepared the manuscript with support from HF and SS. All authors have reviewed and agreed on the manuscript content.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Provenance and peer review Not commissioned; externally peer reviewed.