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Case report
Case of rare association of peripheral neuropathy with mixed connective tissue disorder
  1. Prativa Priyadarshani Sethi1,
  2. Aditya Sudan1,
  3. Suman Kumari2 and
  4. Monika Pathania1
  1. 1Internal Medicine, All India Institute Of Medical Science, Rishikesh, Uttarakhand, India
  2. 2Pathology, All India Institute of Medical Science, Rishikesh, Uttarakhand, India
  1. Correspondence to Dr Monika Pathania; anshupathania27{at}gmail.com

Abstract

Chronic inflammatory demyelinating polyneuropathy (CIDP) is probably the best-recognised progressive immune-mediated peripheral neuropathy. It presents with symmetrical, motor predominant peripheral neuropathy that produces both distal and proximal weakness. Here we report a case of a 38-year-old man who presented with chronic additive large and small joint inflammatory polyarthritis, associated with morning stiffness, anasarca associated with frothy urine and progressive episodic, relapsing and remitting, sensorimotor lower motor neuron type quadriparesis without any bladder and bowel involvement. He was diagnosed as a case of CIDP, and the aetiology was found out to be mixed connective tissue disorder, which is a rare association with CIDP. The patient responded dramatically to glucocorticoid.

  • immunology
  • neurology
  • peripheral nerve disease
  • connective tissue disease

https://doi.org/10.1136/bcr-2020-238519

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    Footnotes

    • Contributors PPS and AS have written the history and under the guidance of treating physician MP, they have thoroughly examined the patient and written the case report. Pathological inputs and compiling was also done by SK.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Competing interests None declared.

    • Provenance and peer review Not commissioned; externally peer reviewed.