Article Text
Abstract
This case report describes a young man with a history of lymphoedema and long-standing gastrointestinal symptoms since childhood. After undergoing extensive investigations, he was diagnosed with primary intestinal lymphangiectasia (IL). The patient’s condition was refractory to conventional medium-chain triglyceride diet but responded well to treatment with subcutaneous octreotide. We have shown octreotide to be effective in improving the pathological effects of primary IL, associated with improved clinical well-being and serology, but it is not a curative therapy.
- gastroenterology
- drugs: gastrointestinal system
- malabsorption
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Footnotes
Contributors AH is the primary author of the case report and has provided input into all sections of the case report. AH was involved in the care of the patient. PY is the patient’s consultant who has had overall responsibility for his investigations, diagnosis and treatment. They are also co-author on the report and have provided input in all sections of the case report. JT is a co-author and was the senior dietician involved in the patient’s care. They have provided input into the treatment of the condition. IH is a co-author on the report and has provided input into all sections of the case report.
Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.
Competing interests None declared.
Provenance and peer review Not commissioned; externally peer reviewed.