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Case report
Growing teratoma syndrome in mixed hepatoblastoma with teratoid features
  1. Sanjeev Khera1,
  2. Vikram Singh2,
  3. Badal Parikh3 and
  4. Karunesh Chand4
  1. 1Pediatrics, Army Hospital Research and Referral, New Delhi, India
  2. 2Pathology, Army Hospital Research and Referral, New Delhi, Delhi, India
  3. 3Anaesthesiology & Critical Care, Army Hospital Research and Referral, New Delhi, India
  4. 4Pediatric Surgery, Army Hospital Research and Referral, New Delhi, India
  1. Correspondence to Dr Sanjeev Khera; kherakherakhera{at}gmail.com

Abstract

Mixed epithelial mesenchymal (MEM) hepatoblastoma with teratoid features is rare histological variant of hepatoblastoma and described in case reports. Growing teratoma syndrome (GTS) is a rare and often unrecognised phenomenon generally associated with less than 5% of germ cell tumour. It is defined by enlarging tumour mass which is generally mature teratoma with normal or significantly decreasing tumour markers during chemotherapy. The treatment outcomes in GTS are dependent on early recognition and complete surgical excision. We describe a rare case of MEM hepatoblastoma with teratoid features with GTS in an infant who had a delay in definitive management due to late diagnosis of GTS.

  • paediatric surgery
  • paediatric oncology

https://doi.org/10.1136/bcr-2020-241197

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    Footnotes

    • Contributors SK provided diagnostic breakthrough, involved with chemotherapeutic management, conceptualised and written manuscript. VS diagnosed the case. KC and BP were involved with surgical management of case. SK and KC are involved with follow up of case.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Competing interests None declared.

    • Patient consent for publication Parental/guardian consent obtained.

    • Provenance and peer review Not commissioned; externally peer reviewed.