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Herlyn-Werner-Wunderlich (HWW) syndrome with kyphoscoliosis: a rare urogenital anomaly in a teenage girl
  1. Manisha Jhirwal1,
  2. Pratibha Singh1,
  3. Charu Sharma1 and
  4. Pushpinder Khera2
  1. 1Obstetrics & Gynecology, AIIMS Jodphur, Jodhpur, Rajasthan, India
  2. 2Radio diagnosis, AIIMS Jodphur, Jodhpur, Rajasthan, India
  1. Correspondence to Dr Manisha Jhirwal; jhirwalm{at}aiimsjodhpur.edu.in

Abstract

The obstructed haemivagina with ipsilateral renal agenesis (OHVIRA) syndrome also known as Herlyn-Werner-Wunderlich syndrome, a rare congenital malformation in females, results due to developmental abnormality in the müllerian duct. We are reporting a case of a 14-year-old girl who presented with pain and a lump in abdomen for the last 5 months. The MRI abdomen and pelvis confirmed the diagnosis of OHVIRA syndrome. The patient underwent haematocolpos and haematometra drainage, followed by vaginal septum resection.

  • obstetrics and gynaecology
  • musculoskeletal and joint disorders
  • radiology (diagnostics)

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Footnotes

  • Contributors MJ prepared the manuscript. CS helped in preparing manuscript, did proof reading. PS did proof reading. PK provided the MRI film and report.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Patient consent for publication Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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