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Sjögren-related cardiomyopathy presenting with cardiogenic shock
  1. Yahia Al Turk1,
  2. Alejandro Lemor2,3,
  3. Mohamed Fayed4 and
  4. Henry Kim2
  1. 1Internal Medicine, Henry Ford Health System, Detroit, Michigan, USA
  2. 2Cardiovascular Medicine, Henry Ford Health System, Detroit, Michigan, USA
  3. 3Centro de Investigación de Epidemiología Clínica y Medicina Basada en la Evidencia, Universidad de San Martín de Porres Facultad de Medicina Humana, La Molina, Peru
  4. 4Anesthesia, Henry Ford Health System, Detroit, Michigan, USA
  1. Correspondence to Dr Yahia Al Turk; yaltur1{at}hfhs.org

Abstract

Previous reports have described non-ischaemic cardiomyopathy related to a variety of autoimmune diseases. However, very few case reports describe Sjögren disease as a contributing factor to cardiomyopathy. We report the case of a 69-year-old woman with a history of Sjögren disease who presented with cardiogenic shock. Laboratory testing and cardiac MRI revealing apical septal late gadolinium enhancement were consistent with an autoimmune aetiology. After ruling out ischaemic, infectious and other possible causes, the patient’s clinical presentation was thought to be related to underlying Sjögren disease. She was treated with intravenous steroids and evidence-based heart failure therapy, but she eventually died after having declined heart transplantation. Given the rarity of Sjögren disease, no diagnostic criteria or standard treatment has been established for cardiomyopathy related to this disease. Diagnosis should be considered in patients who show evidence of autoimmune processes after other possible causes are ruled out.

  • intensive care
  • Sjogren's syndrome
  • cardiovascular medicine
  • heart failure

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Footnotes

  • Contributors YAT formulated the manuscript’s conception and is the main writer of the case and discussion. AL significantly contributed to conception, writing and design. MF contributed to writing and critical revision of the article. HK supervised and critically revised the article.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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