You are here

Article Text

Article menu
Download PDFPDF
Case report
Cystic biliary atresia with congenital absence of portal vein
  1. Ruchira Nandan1,
  2. Manisha Jana2,
  3. Devendra Kumar Yadav1 and
  4. Prabudh Goel1
  1. 1Department of Pediatric Surgery, All India Institute of Medical Sciences, New Delhi, Delhi, India
  2. 2Radiodiagnosis, All India Institute of Medical Sciences (AIIMS), New Delhi, Delhi, India
  1. Correspondence to Dr Devendra Kumar Yadav; drdevendra{at}hotmail.com

Abstract

A 126-day female child presented with jaundice since day 7 of life. She was icteric and had hepatosplenomegaly. Radiological investigations revealed three extrahepatic and multiple intrahepatic biliary cysts, absent gall bladder and portal vein. These findings were confirmed on laparotomy. To the best of our knowledge, this is the first report of cystic biliary atresia associated with congenital absence of portal vein.

  • biliary intervention
  • congenital disorders
  • portal vein
  • paediatric surgery

https://doi.org/10.1136/bcr-2020-239205

Statistics from Altmetric.com

    Request Permissions

    If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.

    View Full Text

    Footnotes

    • Twitter @ drprabudhgoel

    • Contributors The case was admitted under the care of DKY at AIIMS, New Delhi. The case was operated and managed by DKY, RN and PG. The radiological investigations were seen by MJ. The manuscript was written by RN and MJ. DKY and PG helped in the revision of the manuscript. The images were selected and edited by MJ. The revised and final draft has been seen and approved by all authors.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Competing interests None declared.

    • Patient consent for publication Not required.

    • Provenance and peer review Not commissioned; externally peer reviewed.