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Case report
A case of likely acute febrile neutrophilic dermatosis in a 17-year-old male presenting to general paediatrics
  1. Arameh Aghababaie1 and
  2. Richard Patey2
  1. 1Lewisham and Greenwich NHS Foundation Trust, London, UK
  2. 2Children's Services, Medway NHS Foundation Trust, Gillingham, Kent, UK
  1. Correspondence to Dr Arameh Aghababaie; a.aghababaie{at}nhs.net

Abstract

We present the case of a 17-year-old male with a sore throat, tender cervical lymphadenopathy, bilateral erythematous and enlarged tonsils, fever, joint pain, widespread tender purpuric nodules, ulcerative lesions and erythematous pustules. The diagnosis was initially unclear. He had raised neutrophils, erythrocyte sedimentation rate and C-reactive protein. His skin biopsy showed a neutrophilic dermatosis with superficial pustulosis and leukocytoclastic vasculitis. Most likely, the patient suffered from a rare condition called acute febrile neutrophilic dermatosis (AFND). AFND is a very rare disorder of poorly understood aetiology, with only a few hundred reported cases in the literature. The complexity and rarity of this condition, and the difficulty in diagnosing, is an example of the challenge facing paediatricians as the paediatric admission age threshold increases to include older adolescents and young adults up to the age of 25 years, as per the National Health Service (NHS) long-term plan.

  • paediatrics
  • dermatology
  • dermatological
  • disease and health outcomes
  • rheumatology
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Footnotes

  • Contributors AA was involved in the clinical care of the patient, the diagnostic process, the clinical management of the patient, the conception of the case report, data collection and analysis and writing the first draft. RP was involved in the clinical care of the patient, the diagnostic process, the clinical management of the patient, proof-reading and editing the manuscript and supervision.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Patient consent for publication Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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