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Case report
Bilateral superior semicircular canal dehiscence: bilateral conductive hearing loss with subtle vestibular symptoms
  1. Diogo Pereira,
  2. Abílio Leonardo,
  3. Delfim Duarte and
  4. Nuno Oliveira
  1. Otorhinolaryngology, Hospital Pedro Hispano, Matosinhos, Portugal
  1. Correspondence to Dr Diogo Pereira; diogoabreupereira{at}


Superior semicircular canal dehiscence is caused by a bone defect on the roof of the superior semicircular canal. The estimated prevalence when unilateral varies between 0.4% and 0.7% and is still unknown when bilateral. Patients may present with audiologic and vestibular symptoms that may vary from asymptomatic to disabling. We report a case of a 72-year-old Caucasian woman presented to otolaryngology department reporting imbalance, bilateral pulsatile tinnitus, hypoacusis while being very sensitive to certain sounds. Physical examination was unremarkable, except for the Rinne test that was negative in both sides. The patient underwent an audiometry revealing a mild bilateral conductive hearing loss. A temporal bone CT scan was performed which evidenced bilateral superior semicircular canal dehiscence. Cervical vestibular evoked myogenic potentials and electrocochleography confirmed diagnosis. Although rare, superior semicircular canal dehiscence shall be considered in conductive hearing loss with vestibular symptoms.

  • ear, nose and throat/otolaryngology
  • neurootology

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  • Contributors DP and NO: Conception and design, acquisition of data or analysis and interpretation of data; drafting the article or revising it critically for important intellectual content. AL, DD and NO: final approval of the version published; agreement to be accountable for the article and to ensure that all questions regarding the accuracy or integrity of the article are investigated and resolved.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Patient consent for publication Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.