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Rare cause of unilateral upper limb weakness in a young adolescent
  1. Gurinder Kumar and
  2. Andre Prochoroff
  1. Paediatric Neurology, Case Western Reserve University Hospital, Cleveland, Ohio, USA
  1. Correspondence to Dr Gurinder Kumar; kumargurinder{at}


Slowly progressing unilateral upper limb weakness in a previously healthy child can occur due to number of causes which requires a thorough history, physical examination followed by radiological examination, electromyography and so on. Among the various aetiologies, a rare condition such as Hirayama disease is one of the differentials to be considered. There has been a wealth of literature reported on this disease and our case is a learning lesson for all paediatricians to be aware of Hirayama disease and its current concepts.

  • neurology
  • motor neurone disease
  • neuroimaging
  • neuromuscular disease
  • paediatrics

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  • Contributors GK drafted the manuscript and AP managed the patient. AP is guarantor of the manuscript.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Patient consent for publication Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.