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Case report
Primary clear cell sarcoma in the lung apex with spinal metastasis: a fatal outcome
  1. RemyGrace Sass1,
  2. Pavan Kumar Tandra2,
  3. Nicole Shonka2 and
  4. Melissa Manzer3
  1. 1College of Medicine, University of Nebraska Medical Center, Omaha, Nebraska, USA
  2. 2Hematology-Oncology, University of Nebraska Medical Center, Omaha, Nebraska, USA
  3. 3Radiology, University of Nebraska Medical Center, Omaha, Nebraska, USA
  1. Correspondence to Dr Pavan Kumar Tandra; pav.tandra{at}


Clear cell sarcoma (CCS) is a rare tumour that manifests in tendons and aponeuroses of the distal extremities and comprises roughly 1% of all soft tissue cancers. Only two cases of a primary CCS arising in the lung have been reported in the literature, and neither were located in the lung apex. We report a case of a primary CCS located in the lung apex that originally presented as ptosis, as well as arm pain and weakness. Distant metastasis was discovered on diagnosis, which led to irreversible paraplegia and death of the patient.

  • oncology
  • neurology
  • spinal cord

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  • Contributors RGS was the primary author of this case report. She was the primary designer and writer of the report. PKT was the corresponding author. He participated in the planning, writing and editing of the report. NS edited the report. MM participated in the writing of the report and acquisition of images.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Patient consent for publication Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.