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Association between gallbladder agenesis and choledochal cyst: cause or coincidence?
  1. Belén Aneiros Castro1,
  2. Indalecio Cano Novillo2,
  3. Araceli García Vázquez2 and
  4. Mónica De Miguel Moya3
  1. 1 Pediatric Surgery, Hospital Álvaro Cunqueiro, Vigo, Spain
  2. 2 Pediatric Surgery, Hospital Universitario 12 de Octubre, Madrid, Spain
  3. 3 Anesthesiology, Hospital Universitario 12 de Octubre, Madrid, Spain
  1. Correspondence to Dr Belén Aneiros Castro, belenaneiroscastro{at}


This case report describes an extremely rare association between gallbladder agenesis and choledochal cyst (CC). A 9-year-old girl presented with recurrent abdominal pain in the right upper quadrant. Radiological studies revealed a CC type IVa and an agenesis of gallbladder and cystic duct. Due to the possibility of biliary neoplasm, the patient underwent cyst resection and hepaticoduodenostomy. Histopathological findings showed inflamed fibrous tissue covered by biliary epithelium with no evidence of malignancy.

  • biliary intervention
  • congenital disorders

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  • Contributors ICN, BAC and AGV participated in designing the study. BAC, AGV and MDMM participated in gathering the data for the study. ICN and MDMM participated in the analysis of the data. ICN, BAC and AGV wrote the majority of the original draft of the paper. ICN, BAC and MDMM revised the paper critically for important intellectual content. All the authors approved the final version of this paper.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Provenance and peer review Not commissioned; externally peer reviewed.

  • Patient consent for publication Parental/guardian consent obtained.

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