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Rare disease
CASE REPORT
Parkes Weber syndrome presenting as Stewart-Bluefarb acroangiodermatitis
  1. Reena Sharma1,
  2. Mudita Gupta1,
  3. Suresh Thakur2 and
  4. Archit Gupta3
  1. 1 Department of Dermatology, Indira Gandhi Medical College, Shimla, Himachal Pradesh, India
  2. 2 Department of Radiodiagnosis, Indira Gandhi Medical College, Shimla, Himachal Pradesh, India
  3. 3 Department of General Surgery, Indira Gandhi Medical College, Shimla, Himachal Pradesh, India
  1. Correspondence to Dr Archit Gupta, archit9th{at}gmail.com

Abstract

Parkes Weber syndrome (PWS) is a rare disorder characterised by arteriovenous (AV) fistula, along with capillary, lymphatic, venous malformations and limb hypertrophy. Stewart-Bluefarb syndrome is a variant of acroangiodermatitis, which is associated with congenital AV malformation/fistulas. It usually begins early in life, unilaterally over lower extremities presenting as violaceous to dusky coloured macules, papules or plaques with tendency to ulcerate. We are reporting a case of AV malformation fulfilling the triad of PWS and presenting with acroangiodermatitis.

  • dermatology
  • congenital disorders
  • hemangioma
  • vascular surgery

https://doi.org/10.1136/bcr-2018-227793

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    Footnotes

    • Contributors RS: literature search and manuscript preparation; MG: manuscript editing and literature search; ST: radiological literature search and manuscript editing; AG: literature search and manuscript preparation.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Competing interests None declared.

    • Provenance and peer review Not commissioned; externally peer reviewed.

    • Patient consent for publication Parental/guardian consent obtained.