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Case report
Neuro-Sweet disease in a Japanese woman with Sjögren’s syndrome
  1. Tatsuya Kodama1,
  2. Yuki Yamazaki2 and
  3. Hiroaki Takeo3
  1. 1 Department of Internal Medicine, Self Defence Forces Central Hospital, Setagaya-ku, Tokyo, Japan
  2. 2 Department of Dermatology, Self Defence Forces Central Hospital, Setagaya-ku, Tokyo, Japan
  3. 3 Department of Pathology, Self Defence Forces Central Hospital, Setagaya-ku, Tokyo, Japan
  1. Correspondence to Dr Tatsuya Kodama; kodaaman1986{at}


Sweet disease (SD) is a multisystem inflammatory disorder characterised by fever, cutaneous erythematous plaques and aseptic neutrophilic infiltration of various organs. Neuro-Sweet disease (NSD) is a known rare central nervous system complication of SD. We describe a case of a 39-year-old Japanese woman who was diagnosed as NSD associated with Sjögren’s syndrome. She was successfully treated with systemic corticosteroid therapy.

  • headache (including migraines)
  • pathology
  • sjogren's syndrome

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  • Contributors TK wrote the initial draft of the manuscript. YY and HT assisted in the preparation of the manuscript. All authors approved the final version of the manuscript and, agree to be accountable for all aspects of the work in ensuring that questions related to the accuracy or integrity of any part of the work are appropriately investigate and resolved.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Patient consent for publication Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.