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Paediatric presentation of intracranial haemorrhage due to thrombosis of a developmental venous anomaly
  1. Pouya Entezami,
  2. Alan Boulos,
  3. Junichi Yamamoto and
  4. Matthew Adamo
  1. Neurosurgery, Albany Medical Center, Albany, New York, USA
  1. Correspondence to Dr Pouya Entezami, entezap{at}


Developmental venous anomalies (DVAs) are the most commonly encountered cerebral malformations. While generally asymptomatic and discovered as incidental findings, there is a small number that can cause intracranial haemorrhage, usually attributed to associated cavernomas; however, venous thrombosis of the draining vein is a rare cause. A 10-year-old woman presented with seizure episodes. Angiographic evaluation revealed a collection of vessels draining into the superior sagittal sinus via the vein of Trolard, concerning for a DVA. The patient improved clinically with supportive care and antiepileptic treatment. Anatomically, DVAs represent dysplasia of primary capillary beds and smaller cerebral veins, resulting in abnormal venous drainage of the affected parenchyma. Several distinguishing radiological findings can help differentiate a DVA from other pathologies. Early radiological identification can help in the initiation of appropriate therapy and prevent incorrect surgical management leading to further neurological demise.

  • neurosurgery
  • congenital disorders

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  • Contributors All authors have contributed equally to the preparation and submission of this manuscript. All four authors were part of the management team for this patient. With regard to planning, conduct, reporting, acquisition of data, data analysis and interpretation, all four authors (PE, AB, JY and MA) were equally involved. The background information was primarily researched by PE, while drafting of the text was mostly done by PE and MA. Critical review of the manuscript was done by AB and JY, with all authors reviewing and accepting the manuscript in its final form.

  • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

  • Competing interests None declared.

  • Patient consent Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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