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Rare disease
Case report
​Acute airway compromise and coagulopathy: a rare presentation of acquired haemophilia A
  1. William Byron Howden1,2,
  2. Jonathan Kam2,
  3. Nicholas Leith2 and
  4. Shashinder Singh2
  1. 1Discipline of Surgery, The University of Sydney, Sydney, New South Wales, Australia
  2. 2Department of Otolaryngology, Head & Neck Surgery, Gosford Hospital, Gosford, New South Wales, Australia
  1. Correspondence to Dr William Byron Howden; whow4613{at}uni.sydney.edu.au

Abstract

Acquired haemophilia A is a rare but important diagnosis, carrying a mortality rate of 22%. Life-threatening sequalae of this diagnosis includes airway compromise, which can rapidly lead to demise of the patient if left untreated. Our case examines an 80-year-old man presenting with a supraglottic haematoma resulting from acquired haemophilia A causing airway compromise and necessitating definitive airway control. A review of current understanding and management of the disease is also ddiscussed.

  • ear, nose and throat/otolaryngology
  • haematology (incl blood transfusion)
  • adult intensive care

https://doi.org/10.1136/bcr-2019-233345

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    Footnotes

    • Contributors WBH: analysis and interpretation of the case and treatment. Literature review, drafting and revising the work. Final reporting and submission. JK: conception and design, acquisition of data. Literature review, revising the data and case. NL: conception and design, acquisition of data. Supervision. Revise data and case. SS: supervisor of the work. Revision data and case.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Competing interests None declared.

    • Patient consent for publication Not required.

    • Provenance and peer review Not commissioned; externally peer reviewed.