You are here

Article Text

Article menu
Download PDFPDF
Rare disease
CASE REPORT
Mesenchymal chondrosarcoma of maxilla in paediatric patient
  1. Choon Sean Choo1,
  2. Wan Faiziah Wan Abdul Rahman2,3,
  3. Hasnan Jaafar2,3 and
  4. Ramiza Ramza Ramli1,3
  1. 1 Department of Otorhinolaryngology - Head and Neck Surgery, School of Medical Sciences, Universiti Sains Malaysia, Health Campus, Kota Bharu, Kelantan, Malaysia
  2. 2 Department of Pathology, School of Medical Sciences, Universiti Sains Malaysia, Health Campus, Kota Bharu, Kelantan, Malaysia
  3. 3 Hospital Universiti Sains Malaysia, Universiti Sains Malaysia, Kota Bharu, Kelantan, Malaysia
  1. Correspondence to Dr Wan Faiziah Wan Abdul Rahman, wfaiziah{at}usm.my

Abstract

Chondrosarcoma (CS) is a malignant tumour of long and flat bone characterised by the formation of cartilage. Mesenchymal chondrosarcoma (MCS) is a rare subtype of CS that is more aggressive and may lead to erroneous diagnosis in a limited biopsy. The diagnosis is mainly based on the histopathological appearance of biphasic pattern of undifferentiated small round cells separated by islands of well-differentiated hyaline cartilage. We report a case of 13-year-old boy who initially presented with gum swelling and the biopsy result suggested a benign fibrous lesion. Following an extensive lesion shown in radiologic findings, the tumour excision was done and finally was diagnosed as an MCS of the maxilla. The patient was given postoperative chemotherapy (EURO-EWING 99 regimen), and now on regular follow-up for monitoring of local recurrence or tumour metastasis.

  • head and neck cancer
  • pathology
  • head and neck surgery
  • oral and maxillofacial surgery

https://doi.org/10.1136/bcr-2018-228969

Statistics from Altmetric.com

    Request Permissions

    If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.

    View Full Text

    Footnotes

    • Contributors CCS was involved in general drafting and case presentation. WFWAR was involved in drafting the investigation and discussion aspect. HJ was involved in diagnosis and drafting the pathology aspect and RRR was involved in management and reviewing process of the whole article.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Competing interests None declared.

    • Provenance and peer review Not commissioned; externally peer reviewed.

    • Patient consent for publication Not required.